Conditions / Cardiovascular

ankyrin-B-related cardiac arrhythmia

info ยท Cardiovascular

A heart disease characterized by a broad spectrum of cardiac arrhythmias including; bradycardia, sinus arrhythmia, delayed conduction/conduction block, idiopathic ventricular fibrillation, and catecholaminergic polymorphic ventricular tachycardia that has_mate

A heart disease characterized by a broad spectrum of cardiac arrhythmias including; bradycardia, sinus arrhythmia, delayed conduction/conduction block, idiopathic ventricular fibrillation, and catecholaminergic polymorphic ventricular tachycardia that has_material_basis_in heterozygous mutation in the ANK2 gene on chromosome 4q25-q26.

Signs and symptoms

  • Atrial fibrillation
  • Prolonged QT interval
  • Syncope
  • Sudden cardiac death
  • Sinus bradycardia

Also known as: ankyrin-B syndrome