Conditions / Genetic
arrhythmogenic right ventricular dysplasia 4
info · Genetic · ICD-10: I42.8
An arrhythmogenic right ventricular dysplasia associated with variation in the region 2q32.1-q32.3.
Signs and symptoms
- T-wave inversion in the right precordial leads
- Ventricular arrhythmia
- Right ventricular cardiomyopathy
- Focal necrosis of right ventricular muscle cells
- Sudden death
Also known as: ARVC4; ARVD4; arrhythmogenic right ventricular cardiomyopathy 4; familial arrhythmogenic right ventricular dysplasia 4