Conditions / Genetic

arrhythmogenic right ventricular dysplasia 5

info · Genetic · ICD-10: I42.8

An arrhythmogenic right ventricular dysplasia that has_material_basis_in heterozygous mutation in the TMEM43 gene on chromosome 3p25.

Signs and symptoms

  • Premature ventricular contraction
  • Congestive heart failure
  • Chest pain
  • Right ventricular cardiomyopathy
  • Presyncope
  • Palpitations
  • Prolonged QRS complex
  • Ventricular tachycardia
  • Sudden cardiac death
  • Dyskinesia

Also known as: ARVC5; ARVD5; arrhythmogenic right ventricular cardiomyopathy 5; familial arrhythmogenic right ventricular dysplasia 5