Conditions / Genetic

asphyxiating thoracic dystrophy 2

info · Genetic · ICD-10: Q77.2

An asphyxiating thoracic dystrophy that has_material_basis_in homozygous mutation in the IFT80 gene on chromosome 3q25.

Signs and symptoms

  • Mesomelia
  • Short foot
  • Rhizomelia
  • Brachydactyly
  • Postaxial hand polydactyly
  • Short metacarpal
  • Narrow chest
  • Broad palm

Also known as: ATD2; SRTD2; short-rib thoracic dysplasia 2 with or without polydactyly