atrial standstill 1

A heart conduction disease that is characterized by a transient or permanent absence of electrical and mechanical atrial activity and that has_material_basis_in coinheritance of a variant in the SCN5A gene in combination with a rare connexin-40 genotype.

Signs and symptoms

• Atrial standstill
• Ventricular escape rhythm
• Paroxysmal atrial fibrillation
• Endocardial fibroelastosis
• First degree atrioventricular block
• Atrial cardiomyopathy
• Premature atrial contractions