Conditions / Nervous system

autosomal recessive nonsyndromic deafness 101

info · Nervous system · ICD-10: H90.3

An autosomal recessive nonsyndromic deafness that has_material_basis_in mutation in the GRXCR2 gene on chromosome 5q32.

Signs and symptoms

  • Bilateral sensorineural hearing impairment
  • Abnormal vestibular function
  • Visual impairment

Also known as: DFNB101; autosomal recessive deafness 101