Conditions / Nervous system

autosomal recessive nonsyndromic deafness 70

info · Nervous system · ICD-10: H90.3

An autosomal recessive nonsyndromic deafness that has_material_basis_in mutation in the PNPT1 gene on chromosome 2p16.

Signs and symptoms

  • Hearing impairment
  • Abnormal vestibular function
  • Cognitive impairment

Also known as: DFNB70; autosomal recessive deafness 70