Conditions / Syndrome

Bardet-Biedl syndrome 6

info · Syndrome · ICD-10: Q87.89

A Bardet-Biedl syndrome that has_material_basis_in homozygous or compound heterozygous mutation in the MKKS gene on chromosome 20p12.

Signs and symptoms

  • Pigmentary retinopathy
  • Postaxial polydactyly
  • Obesity
  • Intellectual disability
  • Diabetes mellitus
  • External genital hypoplasia
  • Rod-cone dystrophy
  • Syndactyly
  • Hypospadias
  • Renal cyst

Also known as: BBS6