Conditions / Musculoskeletal

Charcot-Marie-Tooth disease dominant intermediate F

info · Musculoskeletal · ICD-10: G60.0

A Charcot-Marie-Tooth disease intermediate type that has_material_basis_in heterozygous mutation in the GNB4 gene on chromosome 3q28.

Signs and symptoms

  • Onion bulb formation
  • Peripheral demyelination
  • Distal lower limb muscle weakness
  • Hammertoe
  • Distal lower limb amyotrophy
  • Absent Achilles reflex
  • Absent patellar reflexes
  • Impaired vibratory sensation
  • Impaired pain sensation
  • Steppage gait

Also known as: CMTDIF; autosomal dominant intermediate Charcot-Marie-Tooth disease type F