Conditions / Musculoskeletal

Charcot-Marie-Tooth disease type 1B

info · Musculoskeletal · ICD-10: G60.0

A Charcot-Marie-Tooth disease type 1 that has_material_basis_in heterozygous mutation in the gene encoding myelin protein zero (MPZ).

Signs and symptoms

  • Decreased motor nerve conduction velocity
  • Distal amyotrophy
  • Distal muscle weakness
  • Distal sensory impairment
  • Pes cavus
  • Areflexia
  • Kyphoscoliosis
  • Peripheral demyelination
  • Steppage gait
  • Ulnar claw

Also known as: CMT1B; Charcot-Marie-Tooth disease slow nerve conduction type linked to Duffy; Charcot-Marie-Tooth neuropathy type 1B; HMSN IB; HMSN1B