Conditions / Musculoskeletal

Charcot-Marie-Tooth disease type 2A2A

info · Musculoskeletal · ICD-10: G60.0

A Charcot-Marie-Tooth disease type 2 that has_material_basis_in heterozygous mutation in the MFN2 gene on chromosome 1p36.22.

Signs and symptoms

  • Hypertonia
  • Axonal degeneration/regeneration
  • Steppage gait
  • Decreased motor nerve conduction velocity
  • Distal amyotrophy
  • Flexion contracture
  • Distal muscle weakness
  • Limb muscle weakness
  • Pain
  • Foot dorsiflexor weakness

Also known as: CMT2A2A; Charcot-Marie-Tooth neuronal type 2A2; Charcot-Marie-Tooth neuropathy type 2A2; HMSN IIA2; HMSN2A2