Conditions / Musculoskeletal

Charcot-Marie-Tooth disease type 2I

info · Musculoskeletal · ICD-10: G60.0

A Charcot-Marie-Tooth disease type 2 that has_material_basis_in heterozygous mutation in the myelin protein-zero gene (MPZ) on chromosome 1q23.

Signs and symptoms

  • Hyporeflexia
  • Axonal degeneration/regeneration
  • Steppage gait
  • Pes cavus
  • Distal amyotrophy
  • Upper limb muscle weakness
  • Areflexia
  • Distal muscle weakness
  • Distal sensory impairment
  • Decreased number of peripheral myelinated nerve fibers

Also known as: CMT2I; Charcot-Marie-Tooth neuropathy type 2I