Conditions / Musculoskeletal

Charcot-Marie-Tooth disease type 4B3

info · Musculoskeletal · ICD-10: G60.0

A Charcot-Marie-Tooth disease type 4 that has_material_basis_in homozygous or compound heterozygous mutation in the SBF1 gene on chromosome 22q.

Signs and symptoms

  • Skeletal muscle atrophy
  • Myelin outfoldings
  • Upper limb muscle weakness
  • Onion bulb formation
  • Areflexia
  • Muscle fibrillation
  • Distal lower limb muscle weakness
  • Lower limb muscle weakness
  • Distal sensory impairment
  • Decreased nerve conduction velocity

Also known as: CMT4B3