Conditions / Genetic

congenital afibrinogenemia

info ยท Genetic

A blood coagulation disease that is characterized by an impaired blood clotting resulting from a lack deficiency of a the fibrinogen protein (coagulation factor I).

Signs and symptoms

  • Abnormal bleeding
  • Afibrinogenemia
  • Prolonged bleeding following circumcision
  • Hypofibrinogenemia
  • Abnormal umbilical stump bleeding
  • Epistaxis
  • Splenic rupture
  • Gingival bleeding
  • Epidural hemorrhage
  • Prolonged bleeding after dental extraction

Also known as: Factor I deficiency; Fibrinogen deficiency