Conditions / Syndrome
cystic fibrosis
info · Syndrome · ICD-10: E84
A syndrome that is characterized by the buildup of thick, sticky mucus that can damage many organs.
Signs and symptoms
- Elevated sweat chloride
- Bronchiectasis
- Decreased forced expiratory flow 25-75%
- Reduced forced expiratory volume in one second
- Chronic sinusitis
- Meconium ileus
- Chronic lung disease
- Male infertility
- Biliary cirrhosis
- Recurrent bronchopulmonary infections
Medications that may treat it
acetylcysteine amiloride dornase alfa ivacaftor
Also known as: CF; mucoviscidosis