desquamative interstitial pneumonia

info · Respiratory · ICD-10: J84.117

An idiopathic interstitial pneumonia that is characterized by the accumulation of bronchiolocentric alveolar macrophages in alveolar spaces and interstitial inflammation and involves mild bronchiolar fibrosis and chronic inflammation.

Signs and symptoms

Desquamative interstitial pneumonitis
Tubulointerstitial fibrosis
Respiratory distress
Type II pneumocyte hypertrophy
Cough
Failure to thrive
Abnormality of metabolism/homeostasis
Respiratory failure
Cor pulmonale
Cyanosis

Also known as: RBILD; familial desquamative interstitial pneumonitis; respiratory bronchiolitis-associated interstitial lung disease