Conditions / Genetic

dilated cardiomyopathy 1E

info · Genetic · ICD-10: I42.0

A dilated cardiomyopathy that has_material_basis_in mutation in the SCN5A gene on chromosome 3p22.2.

Signs and symptoms

  • Reduced left ventricular ejection fraction
  • Atrial standstill
  • Reduced systolic function
  • Atrial flutter
  • Palpitations
  • Premature atrial contractions
  • Syncope
  • Atrioventricular block
  • Dilated cardiomyopathy
  • Atrial fibrillation

Also known as: CDCD2; CMD1E; dilated cardiomyopathy with conduction defect 2; dilated cardiomyopathy with conduction disorder and arrhythmia