Conditions / Syndrome

Duane-radial ray syndrome

info · Syndrome · ICD-10: Q87.8

A syndrome characterized by upper limb anomalies, ocular anomalies, and, in some cases, renal anomalies and that has_material_basis_in heterozygous mutation in the SALL4 gene on chromosome 20q13.

Signs and symptoms

  • Shoulder dislocation
  • Hypoplasia of the radius
  • Hypoplasia of the ulna
  • Microphthalmia
  • Duane anomaly
  • Small thenar eminence
  • Anal stenosis
  • Epicanthus
  • Anal atresia
  • Strabismus

Also known as: DR syndrome; Duane anomaly with radial ray abnormalities and deafness; Okihiro syndrome; acrorenocular syndrome