Conditions / Genetic

galactokinase deficiency

info · Genetic · ICD-10: E74.29

A galactosemia that involves an accumulation of galactose and galactitol secondary to the decreased conversion of galactose to galactose-1-phosphate by galactokinase.

Signs and symptoms

  • Reduced erythrocyte galactokinase activity
  • Galactosuria
  • Hypergalactosemia
  • Cataract
  • Prolonged neonatal jaundice
  • Increased intracranial pressure

Medications that may treat it

lactulose

Also known as: Galactosemia II