Conditions / Infectious
Gerstmann-Straussler-Scheinker syndrome
info · Infectious · ICD-10: A81.82
A prion disease characterized by adult onset of memory loss, dementia, ataxia, and pathologic deposition of amyloid-like plaques in the brain.
Signs and symptoms
- Bradykinesia
- Cerebellar atrophy
- Apraxia
- Gait ataxia
- Rigidity
- Neurofibrillary tangles
- Depression
- Lower limb muscle weakness
- Aggressive behavior
- Emotional lability
Also known as: Gerstmann-Straussler-Scheinker disease; PRION DEMENTIA