Conditions / Immune

hereditary lymphedema II

info · Immune · ICD-10: I89.0

A hereditary lymphedema characterized by onset around puberty of chronic lymphedema particularly in the lower limbs with an apparent autosomal dominant pattern of inheritance.

Signs and symptoms

  • Predominantly lower limb lymphedema
  • Hypoplasia of lymphatic vessels
  • Cleft palate
  • Facial edema
  • Yellow nails

Also known as: LMPH2; Meige disease; Meige lymphedema; late-onset lymphedema; lymphedema preacox