Conditions / Genetic

hereditary spastic paraplegia 46

info · Genetic · ICD-10: G11.4

A hereditary spastic paraplegia that has_material_basis_in mutation in the GBA2 gene on chromosome 9p.

Signs and symptoms

  • Cerebellar atrophy
  • Lower limb spasticity
  • Lower limb muscle weakness
  • Hyperreflexia
  • Cerebral atrophy
  • Babinski sign
  • Hypoplasia of the corpus callosum
  • Dementia
  • Spastic paraplegia
  • Upper limb spasticity

Also known as: SPG46; autosomal recessive spastic paraplegia 46; autosomal recessive spastic paraplegia type 46