Conditions / Genetic

hereditary spastic paraplegia 53

info · Genetic · ICD-10: G11.4

A hereditary spastic paraplegia that has_material_basis_in mutation in the VPS37A gene on chromosome 8p22.

Signs and symptoms

  • Joint hypermobility
  • Kyphosis
  • Lower limb hypertonia
  • Hyperreflexia
  • Pectus carinatum
  • Clonus
  • Delayed speech and language development
  • Upper limb hypertonia
  • Gait disturbance
  • Global developmental delay

Also known as: SPG53; autosomal recessive spastic paraplegia 53; autosomal recessive spastic paraplegia type 53