Conditions / Syndrome

Holt-Oram syndrome

info · Syndrome · ICD-10: Q87.2

A syndrome characterized by congenital anomalies located_in heart and located_in upper limb.

Signs and symptoms

  • Hypoplastic scapulae
  • Short forearm
  • Y-shaped metatarsals
  • Aplasia of the 3rd finger
  • Shield chest
  • Proximal placement of thumb
  • 11 pairs of ribs
  • Distally placed thumb
  • Down-sloping shoulders
  • Sinus bradycardia

Also known as: atrio-digital syndrome; atriodigital dysplasia; heart-hand syndrome