Conditions / Nervous system

hyperekplexia 1

info · Nervous system · ICD-10: G25.8

A hyperekplexia that has_material_basis_in heterozygous, homozygous, or compound heterozygous mutation in the GLRA1 gene on chromosome 5q32.

Signs and symptoms

  • Hypertonia
  • Exaggerated startle response
  • Hypokinesia
  • Inguinal hernia
  • Seizure
  • Nocturnal seizures
  • Hip dislocation
  • Umbilical hernia
  • Aspiration
  • Frequent falls

Also known as: HKPX1