Langerhans-cell histiocytosis

info · Immune · ICD-10: C96.0, C96.6

A histiocytosis that is characterized by clonal proliferation of Langerhans cells.

Signs and symptoms

Encephalopathy
Pulmonary infiltrates
Pallor
Seborrheic dermatitis
Dyspnea
Abdominal distention
Stomatitis
Irritability
Abnormality of the skeletal system
Anemia

Medications that may treat it

Also known as: Histiocytosis X; Langerhan's cell histiocytosis; Langerhans cell granulomatosis; Letterer-Siwe disease; Letterer-Siwe disease involving intra-abdominal lymph nodes