Conditions / Genetic

Leber congenital amaurosis 7

info · Genetic · ICD-10: H35.5

A Leber congenital amaurosis that has_material_basis_in mutation in the CRX gene on chromosome 19q13.

Signs and symptoms

  • Undetectable electroretinogram
  • Nystagmus
  • Visual impairment
  • Keratoconus
  • Cataract
  • Pendular nystagmus
  • Photophobia

Also known as: LCA7