Conditions / Genetic

long QT syndrome 1

info · Genetic · ICD-10: I45.8

A long QT syndrome that has_material_basis_in dominant inheritance of mutation in the KCNQ1 gene on chromosome 11p15.5-p15.4.

Signs and symptoms

  • Syncope
  • Prolonged QTc interval
  • Prolonged QT interval
  • Ventricular fibrillation
  • Torsade de pointes
  • Sudden cardiac death
  • Hearing abnormality

Also known as: LQT1; ventricular fibrillation with prolonged QT interval