Conditions / Syndrome

Meckel syndrome 6

info · Syndrome · ICD-10: Q61.9

A Meckel syndrome that has_material_basis_in an autosomal recessive mutation of the CC2D2A gene on chromosome 4p15.32.

Signs and symptoms

  • Pulmonary hypoplasia
  • Talipes equinovarus
  • Cystic liver disease
  • Hepatic fibrosis
  • Occipital encephalocele
  • Renal cyst
  • Hepatic cysts
  • Postaxial foot polydactyly
  • Postaxial hand polydactyly
  • Cleft palate

Also known as: MKS6; Meckel-Gruber syndrome, type 6