Conditions / Musculoskeletal

MERRF syndrome

info · Musculoskeletal · ICD-10: E88.42

Signs and symptoms

  • Ragged-red muscle fibers
  • Generalized myoclonic seizure
  • Increased circulating pyruvate concentration
  • Seizure
  • Myopathy
  • Sensorineural hearing impairment
  • Increased circulating lactate concentration
  • Ataxia
  • Muscle weakness
  • Spasticity

Also known as: Fukuhara syndrome; Myoclonic epilepsy - ragged red fibers; Myoclonus epilepsy AND ragged red fibers; Myoclonus with epilepsy and with Ragged Red Fibers