Conditions / Genetic

neurodegeneration with brain iron accumulation 4

info · Genetic · ICD-10: G23.0

A neurodegeneration with brain iron accumulation that has_material_basis_in autosomal recessive inheritance of mutation in the C19orf12 gene on chromosome 19q12.

Signs and symptoms

  • Optic atrophy
  • Babinski sign
  • Abnormal pyramidal sign
  • Parkinsonism
  • Dysarthria
  • Generalized dystonia
  • Abnormal lower motor neuron morphology
  • Elevated circulating creatine kinase activity
  • Dystonia
  • Distal amyotrophy

Also known as: MPAN; Mitochondrial Protein-Associated Neurodegeneration; NBIA due to C19orf12 mutation; NBIA4; Neurodegeneration with brain iron accumulation due to C19orf12 mutation