Conditions / Syndrome

oculoauricular syndrome

info · Syndrome · ICD-10: Q87.8

A syndrome characterized by microcornea, microphthalmia, anterior-segment dysgenesis, cataract, coloboma of various parts of the eye, abnormalities of the retinal pigment epithelium, and rod-cone dystrophy and a particular cleft ear lobule.

Signs and symptoms

  • Cataract
  • Developmental cataract
  • Iris coloboma
  • Posterior embryotoxon
  • Microphthalmia
  • Low-set ears
  • Microphakia
  • Morning glory anomaly
  • Microcornea
  • Sclerocornea