Conditions / Genetic

osteogenesis imperfecta type 9

info · Genetic · ICD-10: Q78.0

An osteogenesis imperfecta that has_material_basis_in mutation in the PPIB gene on chromosome 15q22.

Signs and symptoms

  • Wide anterior fontanel
  • Finger joint hypermobility
  • Disproportionate short-limb short stature
  • Recurrent fractures
  • Narrow chest
  • Pes planus
  • Flat occiput
  • Bowing of limbs due to multiple fractures
  • Blue sclerae
  • Delayed gross motor development

Also known as: OI9; osteogenesis imperfecta type IX