Conditions / Skin

pityriasis rubra pilaris

info · Skin · ICD-10: L44.0

A skin disease that is characterized by hyperkeratotic follicular papules coalescing into orange-red scaly plaques, islands of sparing, and palmoplantar keratoderma.

Signs and symptoms

  • Subungual hyperkeratosis
  • Erythematous plaque
  • Parakeratosis
  • Keratosis pilaris
  • Hypergranulosis
  • Orthokeratosis
  • Palmoplantar keratoderma
  • Ectropion

Also known as: Devergie's disease