Conditions / Nervous system

pontocerebellar hypoplasia type 8

info · Nervous system · ICD-10: Q04.3

A pontocerebellar hypoplasia that is characterized by delayed psychomotor development, chorea, hypotonia, spasticity and visual defects, has_material_basis_in autosomal recessive inheritance of mutation in the CHMP1A gene.

Signs and symptoms

  • Global developmental delay
  • Reduced cerebral white matter volume
  • Hypoplasia of the corpus callosum
  • Cerebellar hypoplasia
  • Reduced social responsiveness
  • Poor speech
  • Intellectual disability
  • Absent speech
  • Dysphagia
  • Delayed ability to walk