Conditions / Syndrome

primary ciliary dyskinesia 1

info · Syndrome · ICD-10: Q34.8

A primary ciliary dyskinesia that is characterized by autosomal recessive inheritance with outer dynein arm defect and in about half of patients situs inversus and has_material_basis_in compound heterozygous mutation in the DNAI1 gene on chromosome 9p13.

Signs and symptoms

  • Chronic sinusitis
  • Atelectasis
  • Absent outer dynein arms
  • Immotile cilia
  • Recurrent bronchitis
  • Chronic otitis media
  • Chronic rhinitis
  • Situs inversus totalis
  • Bronchiectasis
  • Male infertility

Also known as: CILD1; primary ciliary dyskinesia 1 with or without situs inversus