Conditions / Syndrome

primary ciliary dyskinesia 6

info · Syndrome · ICD-10: Q34.8

A primary ciliary dyskinesia that is characterized by partial outer dynein arm defect and has_material_basis_in mutation in the TXNDC3 gene on the chromosome 7p14.1.

Signs and symptoms

  • Ciliary dyskinesia
  • Absent/shortened outer dynein arms
  • Abnormal ciliary motility
  • Abnormal respiratory motile cilium morphology
  • Sinusitis
  • Recurrent respiratory infections
  • Recurrent sinusitis

Also known as: CILD6