Conditions / Syndrome

primary ciliary dyskinesia 9

info · Syndrome · ICD-10: Q34.8

A primary ciliary dyskinesia that is characterized by autosomal recessive inheritance with outer dynein arm defect, neonatal respiratory distress, sinusitis, otitis, bronchiectasis, and variable occurence of laterality defects and has_material_basis_in homozyg

A primary ciliary dyskinesia that is characterized by autosomal recessive inheritance with outer dynein arm defect, neonatal respiratory distress, sinusitis, otitis, bronchiectasis, and variable occurence of laterality defects and has_material_basis_in homozygous mutation in the DNAI2 gene on chromosome 17q25.

Signs and symptoms

  • Decreased nasal nitric oxide
  • Chronic sinusitis
  • Absent outer dynein arms
  • Recurrent otitis media
  • Chronic otitis media
  • Bronchiectasis
  • Neonatal respiratory distress
  • Situs inversus totalis
  • Chronic rhinitis
  • Male infertility

Also known as: CILD9; primary ciliary dyskinesia 9 with or without situs inversus