Conditions / Genetic

Renpenning syndrome

info · Genetic · ICD-10: Q87.5

An intellectual disability that is characterized by small head size (microcephaly), long narrow face, short stature, small testes, and intellectual deficit which follows X-linked inheritance and presents most often in males.

Signs and symptoms

  • Global developmental delay
  • Microcephaly
  • Short philtrum
  • Narrow face
  • Short stature
  • Cupped ear
  • Cataract
  • Intellectual disability
  • Poor suck
  • Camptodactyly

Also known as: Golabi-Ito-Hall syndrome; Sutherland-Haan X-linked mental retardation syndrome; X-linked intellectual disability due to PQBP1 mutations; X-linked intellectual disability, Renpenning type; X-linked mental retardation Renpenning type