scimitar syndrome

A congenital heart disease that is characterized by partial or entire anomalous curved venous drainage of the right lung to the inferior vena cava, association with variable right lung and pulmonary artery hypoplasia, dextraposition of the heart and an anomalo

A congenital heart disease that is characterized by partial or entire anomalous curved venous drainage of the right lung to the inferior vena cava, association with variable right lung and pulmonary artery hypoplasia, dextraposition of the heart and an anomalous systemic blood supply to the ipsilateral lung.

Signs and symptoms

• Dextrocardia
• Pulmonary arterial hypertension
• Recurrent respiratory infections
• Total anomalous pulmonary venous return

Also known as: Halasz syndrome; congenital venolobar syndrome; hypogenetic lung syndrome; mirror-image lung syndrome; pulmonary venolobar syndrome