Conditions / Cardiovascular

Sturge-Weber syndrome

info · Cardiovascular · ICD-10: Q85.89

A vascular disease characterized by intracranial vascular anomaly, leptomeningeal angiomatosis, facial cutaneous vascular malformations, and glaucoma that has_material_basis_in somatic mutation in the GNAQ gene on chromosome 9q21.2.

Signs and symptoms

  • Arachnoid hemangiomatosis
  • Seizure
  • Cerebral cortical atrophy
  • Buphthalmos
  • Choroidal hemangioma
  • Facial hemangioma
  • Macrocephaly
  • Intellectual disability

Also known as: SWS; Sturge-Weber-Dimitri syndrome; Sturge-Weber-Krabbe angiomatosis; Sturge-Weber-Krabbe syndrome; encephalofacial angiomatosis