Conditions / Genetic

syndromic X-linked intellectual disability Raymond type

info · Genetic · ICD-10: Q87.8

A syndromic X-linked intellectual disability characterized by intellectual disability and marfanoid habitus that has_material_basis_in mutation in the ZDHHC9 gene on chromosome Xq26.1.

Signs and symptoms

  • Intellectual disability
  • Arachnodactyly
  • Joint contracture of the 5th finger
  • Strabismus
  • Disproportionate tall stature
  • Pectus carinatum
  • Protruding ear
  • Pes planus
  • Atypical behavior

Also known as: MRXSR; X-linked syndromic intellectual developmental disorder Raymond type; mental retardation, X-linked syndromic, Raymond type