Conditions / Syndrome

Usher syndrome type 2A

info · Syndrome · ICD-10: H35.5

An Usher syndrome type 2 characterized by moderate to severe sensorineural hearing loss, mainly affecting perception of high frequency sounds and progressive retinitis pigmentosa that has_material_basis_in homozygous or compound heterozygous mutation in the US

An Usher syndrome type 2 characterized by moderate to severe sensorineural hearing loss, mainly affecting perception of high frequency sounds and progressive retinitis pigmentosa that has_material_basis_in homozygous or compound heterozygous mutation in the USH2A gene on chromosome 1q41.

Signs and symptoms

  • Rod-cone dystrophy
  • Congenital sensorineural hearing impairment

Also known as: USH2A; Usher syndrome type IIA