Conditions / Eye

vitelliform macular dystrophy

info · Eye · ICD-10: H35.5

A macular degeneration that it is characterized by the disruption of cells in a small area near the center of the retina, the macula and may cause progressive vision loss.

Signs and symptoms

  • Metamorphopsia
  • Reduced visual acuity
  • Visual impairment
  • Vitelliform macular lesion
  • Decreased Arden ratio of electrooculogram
  • Moderately reduced visual acuity
  • Subretinal fluid
  • Cystoid macular degeneration
  • Macular dystrophy
  • Abnormal electroretinogram

Also known as: Best disease; Best macular dystrophy; juvenile-onset vitelliform macular dystrophy