Conditions / Syndrome

Williams-Beuren syndrome

info · Syndrome · ICD-10: Q93.82

A syndrome that is characterized by mild to moderate intellectual disability, a broad forehead, a short nose with a broad tip, full cheeks, and a wide mouth with full lips and difficulty with visual-spatial tasks and has_material_basis_in hemizygous deletion o

A syndrome that is characterized by mild to moderate intellectual disability, a broad forehead, a short nose with a broad tip, full cheeks, and a wide mouth with full lips and difficulty with visual-spatial tasks and has_material_basis_in hemizygous deletion of 1.5 to 1.8 Mb on chromosome 7q11.23.

Signs and symptoms

  • Anxiety
  • Incoordination
  • Supravalvular aortic stenosis
  • Diabetes mellitus
  • Failure to thrive in infancy
  • Strabismus
  • Short stature
  • Short nose
  • Gastroesophageal reflux
  • Gait imbalance

Also known as: Fanconi Schlesinger syndrome; WBS